《英文msh词典》Disease,Caroli's
[入口词] Disease,Caroli's
[主题词] Caroli Disease
[英文释义] Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS,INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION,PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.