《英文msh词典》Glanzmann Thrombasthenia
[同义词] Glanzmann Thrombasthenia
[主题词] Thrombasthenia
[中文释义] Glanzmann血小板机能不全
[英文释义] A congenital bleeding disorder with prolonged bleeding time,absence of aggregation of platelets in response to most agents,especially ADP,and impaired or absent clot retraction. Platelet membranes are deficient in or have a defect in the glycoprotein IIb-IIIa complex (PLATELET GLYCOPROTEIN GPIIB-IIIA COMPLEX).