单词 | Anemia,Dyserythropoietic,Congenital |
释义 | Anemia,Dyserythropoietic,Congenital《英文msh词典》Anemia,Dyserythropoietic,Congenital [主题词] Anemia,Dyserythropoietic,Congenital [同义词] Dyserythropoietic Anemia,Congenital [同义词] HEMPAS [入口词] Anemia,Congenital Dyserythropoietic [入口词] Anemia,Dyserythropoietic,Congenital,Type II [入口词] Congenital Dyserythropoietic Anemia [入口词] Anemias,Congenital Dyserythropoietic [入口词] Congenital Dyserythropoietic Anemias [入口词] Dyserythropoietic Anemias,Congenital [中文释义] 贫血,红细胞生成障碍性,先天性 [英文释义] A familial disorder characterized by anemia with multinuclear erythroblasts,karyorrhexis,asynchrony of nuclear and cytoplasmic maturation,and various nuclear abnormalities of bone marrow erythrocyte precursors. Type II is the most common of the 3 types of congenital dyserythropoietic anemia; it is often referred to as HEMPAS,based on the Hereditary Erythroblast Multinuclearity with Positive Acidified Serum test. |
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