《英文msh词典》Immunologic Deficiency,Severe Combined
[入口词] Immunologic Deficiency,Severe Combined
[主题词] Severe Combined Immunodeficiency
[英文释义] Group of rare congenital disorders characterized by impairment of both humoral and cell-mediated immunity,leukopenia,and low or absent antibody levels. It is inherited as an X-linked or autosomal recessive defect. About half of the patients with autosomal recessive SCID are deficient in the enzyme adenosine deaminase.