《英文msh词典》Lymphohistiocytosis,Hemophagocytic
[同义词] Lymphohistiocytosis,Hemophagocytic
[主题词] Histiocytosis,Non-Langerhans-Cell
[中文释义] 淋巴组织细胞增多症,嗜血细胞性
[英文释义] Group of disorders which feature accumulations of active histiocytes and lymphocytes,but where the histiocytes are not Langerhans cells. The group includes hemophagocytic lymphohistiocytosis,infection-associated hemophagocytic syndrome,sinus histiocytosis,xanthogranuloma,reticulohistiocytoma,juvenile xanthoma,xanthoma disseminatum,as well as the lipid storage diseases (sea-blue histiocyte syndrome and Niemann-Pick disease).