《英文msh词典》Papillon Lefevre Syndrome
[入口词] Papillon Lefevre Syndrome
[主题词] Papillon-Lefevre Disease
[英文释义] Rare,autosomal recessive disorder occurring between the first and fifth years of life. It is characterized by palmoplantar keratoderma with periodontitis followed by the premature shedding of both deciduous and permanent teeth.