单词 | Syndromes,Leukocyte-Adhesion Deficiency |
释义 | Syndromes,Leukocyte-Adhesion Deficiency《英文msh词典》Syndromes,Leukocyte-Adhesion Deficiency [入口词] Syndromes,Leukocyte-Adhesion Deficiency [主题词] Leukocyte-Adhesion Deficiency Syndrome [英文释义] Rare,autosomal recessive disorder caused by deficiency of the beta 2 integrin receptors (RECEPTORS,LEUKOCYTE-ADHESION) comprising the CD11/CD18 family of glycoproteins. The syndrome is characterized by abnormal adhesion-dependent functions,especially defective tissue emigration of neutrophils,leading to recurrent infection. |
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