《英文msh词典》Trihexosides,Ceramide
[入口词] Trihexosides,Ceramide
[主题词] Trihexosylceramides
[英文释义] Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue,due to a defect in ceramide trihexosidase,is the cause of angiokeratoma corporis diffusum (FABRY DISEASE).