《英文msh词典》beta D Mannosidase
[入口词] beta D Mannosidase
[主题词] beta-Mannosidase
[英文释义] An enzyme that catalyzes the hydrolysis of terminal,non-reducing beta-D-mannose residues in beta-D-mannosides. The enzyme plays a role in the lysosomal degradation of the N-glycosylprotein glycans. Defects in the lysosomal form of the enzyme in humans result in a buildup of mannoside intermediate metabolites and the disease BETA-MANNOSIDOSIS.